ABSTRACT

Sturge Weber Syndrome (SWS), also known as encephalotrigeminal angiomatosis, is a rare neurocutaneous syndrome which is characterized by a classical clinical triad of Port-wine stain of the face, epilepsy and glaucoma. Other most common symptoms are mental retardation, headache, behavioral disorders and visual field defects. Neuroimaging provides important information for understanding the underlying pathology of symptoms. Computed Tomography (CT) and Magnetic Resonance Imaging (MRI) are commonly used imaging modalities. Among them, MRI is the best modality for assesment of neurologic involvement such as leptomeningeal angiomatosis. Furthermore, recent advances in MRI allow assesment of subtle microstructural brain changes that cannot be detected on conventional MRI images. We report three adult patients with SWS with their CT and MRI findings.

Keywords: Sturge Weber Syndrome, Brain CT, Brain MRI